Case Report
Primary Cutaneous Ewing Sarcoma: Case Report and Review of Literature
Jlalia Z1*, Sboui I2, Bouhajja L2, Abid L2, Smida M2, Klibi F2 and Daghfous MS21Department of Anatomopathology, Kassab institute of orthopedic surgery, Ksar said, Tunisia
2Department of Kassab institute, University of Tunis, El Manar, Ksar said, Tunisia
- *Corresponding Author:
- Jlalia Z
Department of Orthopedic and traumatology
Kassab institute of orthopedic surgery
Ksar said 2010 Tunis, Tunisia
Tel: +00 216 95562337
E-mail: sboui_imedk@yahoo.fr
Received date: January 28, 2016; Accepted date: February 04, 2017; Published date: February 10, 2017
Citation: Jlalia Z, Sboui I, Bouhajja L, Abid L, Smida M, et al. (2017) Primary Cutaneous Ewing Sarcoma: Case Report and Review of Literature. J Orthop Oncol 3:115. doi: 10.4172/2472-016X.1000115
Copyright: © 2017 Jlalia Z, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
Abstract
Ewing sarcoma (ES) is a primitive neuroectodermal tumor. It’s usually a primary bone tumor but rarely occurs in the skin and subcutaneous tissues. Current literature reports only a few isolated cases or small series. To date, less than 100 cases have been reported. The diagnosis is made by aspiration cytology, histochemical stains, immunohistochemistry, electron microscopy, cytogenetics and molecular genetics of translocations. Cutaneous ES has better prognosis than primary bone or soft tissue ES with a survival rate of 91% in 10 years. The presence of metastasis is really rare. Currently, no specific recommendations to primitively cutaneous Ewing tumors, these latter are treated as bone Ewing's sarcomas: neoadjuvant chemotherapy, surgery, adjuvant chemotherapy (+/− radiotherapy), and autologous bone marrow transplantation in high risk patients. We report a new case in a 20-yearold female with a lesion in the left elbow.
